Aneurisma de artéria pulmonar como apresentação clínica de uma doença de Behçet: a propósito de um caso

Abstract

Objective: To present clinical aspects and radiological changes observed in a case of Behçet’s disease. Methodology: The research was conducted through the investigation of a patient diagnosed with Behçet’s disease presenting with pulmonary artery aneurysm. Case description: Patient with a history of recurrent painful oral and genital ulcers. He presented with edema and pain in the cervical region, being diagnosed with internal jugular vein thrombosis and right brachiocephalic vein. The patient developed dyspnea, chest pain, hemoptysis, hematemesis, and pulmonary artery aneurysm was diagnosed, as well as painful ulcers, and Behçet’s disease was diagnosed. Discussion: From the International Study Group for Behçet’s Disease classification, the presence of recurrent oral ulcers and two of the following alterations - genital ulcers, typical eye lesions (uveitis, retinal vasculitis), characteristic skin lesions, or a positive patergia test define the diagnosis of Behçet’s disease. Although rare, affecting less than 5% of patients, pulmonary artery involvement is the most feared form of vascular complication. Conclusion: We can conclude that it is important to consider the diagnosis of Behçet, as this pathology can affect several vessels of any caliber in the body and may result in thrombophlebitis, arterial stenosis, occlusions and aneurysms.