Síndrome de ehlers-danlos: relato de caso de gêmeas univitelinas pós-correção ortodôntica.

Abstract

Objective: This article aims to report the main conservative clinical, radiographic and orthodontic aspects in univiteline twins born to healthy parents who present with Ehlers-Danlos syndrome (EDS). Case report: Ten-year-old univiteline twins with EDS presented for oral evaluation. Radiographically, some deciduous molars presented exfoliation, caries and lateral agenesis. Lateral cephalogram showed malocclusion in both sisters. The intraoral examination revealed presence of lip and lingual frenulum of both patients. The dental treatment consisted of restorative and preventive procedures, as well as exodontias of deciduous and supernumerary teeth. The orthodontic fixed appliance was first used for transverse and vertical corrections, using light and constant forces, and a periodontal safety monitoring was performed. A second orthodontic moment will be performed at the end of the child's growth and development period to make room for the installation of future implants of the absent upper lateral incisors. Conclusion: The orthodontic treatment of this rare case of univiteline twins with EDS was able to be performed without complications to the periodontal support of the teeth, since it was carried out conservatively in children. The presence of lip and lingual frenulum was observed in the case. Therefore, new studies should be performed to prove better orthodontic conduction in classical cases of EDS, as well as studies to re-evaluate the absence of lip and / or lingual frenulum as a clinical sign of the syndrome.